TABLE 2.
Cause of death in patients with refractory celiac disease
Cause of death | Refractory Celiac Disease Type I (n=8) |
Refractory Celiac Disease Type II (n=7) |
---|---|---|
Refractory state itself | 5 | 0 |
Enteropathy-associated T-cell lymphoma | 0 | 6 |
Other celiac disease-related | 0 | 0 |
Other celiac disease-unrelated | 3* | 1** |
Giant cell myocarditis, progressive Creutzfeldt-Jacob disease-like neurologic disorder, invasive aspergillosis
Unexplained multiple organ failure